Background and Importance: Hemangioblastomas (HBL) are tumors constantly present in the neurosurgeon's daily life, affecting mainly the posterior fossa region. In patients with von Hippel-Lindau, their presence is even more striking. However, the authors, through a report of a case with the literature review, show that hemangioblastomas should also be part of the range of differential diagnoses of supratentorial lesions even in patients not carrying the genetic mutation. Clinical Presentation: A 45-year-old male patient has a 2 weeks history of headache associated with nauseas and vertigo. In the last two weeks the pain was being progressively more frequently with increase in intensity and duration. At examination he was oriented, with face of pain, muscle examination was normal as all the neurological examination. The patient was submitted to a Magnetic Resonance (MR) of the brain that showed an expansive lesion in the brain located in the left frontal lobe, adjacent to the medial line with moderated adjacent edema and with gadolinium injection the tumor was heterogeneous almost solid with cystic parts and including adjacent impregnation of the dura of the midline. Surgical treatment was done. The lesion was completed resected including the dura of the convexity that was invaded by the tumor. Postoperative period was uneventful, with resolution of the headache and no deficits. Patient was discharged 3 days after surgery. Pathology reveals the lesion was a hemangioblastoma. Patient made genetic exams and confirms that didn’t have Von Hippel Lindau disease. MR of the brain, almost 3 years of the surgery, reveals no tumor. Conclusion: Hemangioblastoma is a rare tumor, especially in its supratentorial location. However, this case reflects the importance of including HBL as a differential diagnostic allowing a better therapeutic planning, ensuring better prognosis and facilitating their treatment.
| Published in | International Journal of Neurosurgery (Volume 5, Issue 1) |
| DOI | 10.11648/j.ijn.20210501.11 |
| Page(s) | 1-3 |
| Creative Commons |
This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited. |
| Copyright |
Copyright © The Author(s), 2021. Published by Science Publishing Group |
Hemangioblastoma, Supratentorial, Von Hippel Lindau, Brain Tumor
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APA Style
Jose Carlos Rodrigues Junior, Vithor Ely Bortholin da Silva, Roberto Bezerra Vital, Renan Luiz Lapate, Marcelo Ferraz Campos. (2021). Supratentorial Hemangioblastomas Without Von - Hippel Lindau Disease – Case Report and Review. International Journal of Neurosurgery, 5(1), 1-3. https://doi.org/10.11648/j.ijn.20210501.11
ACS Style
Jose Carlos Rodrigues Junior; Vithor Ely Bortholin da Silva; Roberto Bezerra Vital; Renan Luiz Lapate; Marcelo Ferraz Campos. Supratentorial Hemangioblastomas Without Von - Hippel Lindau Disease – Case Report and Review. Int. J. Neurosurg. 2021, 5(1), 1-3. doi: 10.11648/j.ijn.20210501.11
AMA Style
Jose Carlos Rodrigues Junior, Vithor Ely Bortholin da Silva, Roberto Bezerra Vital, Renan Luiz Lapate, Marcelo Ferraz Campos. Supratentorial Hemangioblastomas Without Von - Hippel Lindau Disease – Case Report and Review. Int J Neurosurg. 2021;5(1):1-3. doi: 10.11648/j.ijn.20210501.11
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Download@article{10.11648/j.ijn.20210501.11,
author = {Jose Carlos Rodrigues Junior and Vithor Ely Bortholin da Silva and Roberto Bezerra Vital and Renan Luiz Lapate and Marcelo Ferraz Campos},
title = {Supratentorial Hemangioblastomas Without Von - Hippel Lindau Disease – Case Report and Review},
journal = {International Journal of Neurosurgery},
volume = {5},
number = {1},
pages = {1-3},
doi = {10.11648/j.ijn.20210501.11},
url = {https://doi.org/10.11648/j.ijn.20210501.11},
eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ijn.20210501.11},
abstract = {Background and Importance: Hemangioblastomas (HBL) are tumors constantly present in the neurosurgeon's daily life, affecting mainly the posterior fossa region. In patients with von Hippel-Lindau, their presence is even more striking. However, the authors, through a report of a case with the literature review, show that hemangioblastomas should also be part of the range of differential diagnoses of supratentorial lesions even in patients not carrying the genetic mutation. Clinical Presentation: A 45-year-old male patient has a 2 weeks history of headache associated with nauseas and vertigo. In the last two weeks the pain was being progressively more frequently with increase in intensity and duration. At examination he was oriented, with face of pain, muscle examination was normal as all the neurological examination. The patient was submitted to a Magnetic Resonance (MR) of the brain that showed an expansive lesion in the brain located in the left frontal lobe, adjacent to the medial line with moderated adjacent edema and with gadolinium injection the tumor was heterogeneous almost solid with cystic parts and including adjacent impregnation of the dura of the midline. Surgical treatment was done. The lesion was completed resected including the dura of the convexity that was invaded by the tumor. Postoperative period was uneventful, with resolution of the headache and no deficits. Patient was discharged 3 days after surgery. Pathology reveals the lesion was a hemangioblastoma. Patient made genetic exams and confirms that didn’t have Von Hippel Lindau disease. MR of the brain, almost 3 years of the surgery, reveals no tumor. Conclusion: Hemangioblastoma is a rare tumor, especially in its supratentorial location. However, this case reflects the importance of including HBL as a differential diagnostic allowing a better therapeutic planning, ensuring better prognosis and facilitating their treatment.},
year = {2021}
}
TY - JOUR T1 - Supratentorial Hemangioblastomas Without Von - Hippel Lindau Disease – Case Report and Review AU - Jose Carlos Rodrigues Junior AU - Vithor Ely Bortholin da Silva AU - Roberto Bezerra Vital AU - Renan Luiz Lapate AU - Marcelo Ferraz Campos Y1 - 2021/01/04 PY - 2021 N1 - https://doi.org/10.11648/j.ijn.20210501.11 DO - 10.11648/j.ijn.20210501.11 T2 - International Journal of Neurosurgery JF - International Journal of Neurosurgery JO - International Journal of Neurosurgery SP - 1 EP - 3 PB - Science Publishing Group SN - 2640-1959 UR - https://doi.org/10.11648/j.ijn.20210501.11 AB - Background and Importance: Hemangioblastomas (HBL) are tumors constantly present in the neurosurgeon's daily life, affecting mainly the posterior fossa region. In patients with von Hippel-Lindau, their presence is even more striking. However, the authors, through a report of a case with the literature review, show that hemangioblastomas should also be part of the range of differential diagnoses of supratentorial lesions even in patients not carrying the genetic mutation. Clinical Presentation: A 45-year-old male patient has a 2 weeks history of headache associated with nauseas and vertigo. In the last two weeks the pain was being progressively more frequently with increase in intensity and duration. At examination he was oriented, with face of pain, muscle examination was normal as all the neurological examination. The patient was submitted to a Magnetic Resonance (MR) of the brain that showed an expansive lesion in the brain located in the left frontal lobe, adjacent to the medial line with moderated adjacent edema and with gadolinium injection the tumor was heterogeneous almost solid with cystic parts and including adjacent impregnation of the dura of the midline. Surgical treatment was done. The lesion was completed resected including the dura of the convexity that was invaded by the tumor. Postoperative period was uneventful, with resolution of the headache and no deficits. Patient was discharged 3 days after surgery. Pathology reveals the lesion was a hemangioblastoma. Patient made genetic exams and confirms that didn’t have Von Hippel Lindau disease. MR of the brain, almost 3 years of the surgery, reveals no tumor. Conclusion: Hemangioblastoma is a rare tumor, especially in its supratentorial location. However, this case reflects the importance of including HBL as a differential diagnostic allowing a better therapeutic planning, ensuring better prognosis and facilitating their treatment. VL - 5 IS - 1 ER -
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