The constitutional deficiency in factor VII (FVII) of the coagulation is a rare autosomal recessive disease, responsible for a hemorrhagic syndrome of variable intensity poorly correlated with plasma levels of FVII. This deficit is suspected in front of an isolated reduction in the rate of prothrombine and confirmed by the dosage of this factor. We report a case of congenital FVII deficiency in a patient aged 22 years, who underwent surgical treatment of nephrolithiasis. FVII deficiency was 22%, no replacement therapy was introduced to the patient, and no bleeding complications were observed in intraoperative or postoperative. In conclusion, the perioperative transfusion with fresh frozen plasma (FFP) or the contribution of FVII in a patient with a moderate deficit in FVII is not systematic, and it cannot be considered if there is a risk of bleeding or in case of deficiency of FVII.
| Published in | Journal of Anesthesiology (Volume 1, Issue 3) |
| DOI | 10.11648/j.ja.20130103.12 |
| Page(s) | 24-26 |
| Creative Commons |
This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited. |
| Copyright |
Copyright © The Author(s), 2013. Published by Science Publishing Group |
Anesthesia, Coagulation, Congenital Deficiency, Factor VII, Hemorrhage
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APA Style
Hicham Bakkali, Salahedine Massou, Fayçal Labrini, Khalil Mounir, Mustapha Bensghir, et al. (2013). Congenital Deficiency in Factor VII of the Coagulation and the Anesthesia. International Journal of Anesthesia and Clinical Medicine, 1(3), 24-26. https://doi.org/10.11648/j.ja.20130103.12
ACS Style
Hicham Bakkali; Salahedine Massou; Fayçal Labrini; Khalil Mounir; Mustapha Bensghir, et al. Congenital Deficiency in Factor VII of the Coagulation and the Anesthesia. Int. J. Anesth. Clin. Med. 2013, 1(3), 24-26. doi: 10.11648/j.ja.20130103.12
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Download@article{10.11648/j.ja.20130103.12,
author = {Hicham Bakkali and Salahedine Massou and Fayçal Labrini and Khalil Mounir and Mustapha Bensghir and Hicham Azendour and Hicham Balkhi and Charqui Haimeur},
title = {Congenital Deficiency in Factor VII of the Coagulation and the Anesthesia},
journal = {International Journal of Anesthesia and Clinical Medicine},
volume = {1},
number = {3},
pages = {24-26},
doi = {10.11648/j.ja.20130103.12},
url = {https://doi.org/10.11648/j.ja.20130103.12},
eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ja.20130103.12},
abstract = {The constitutional deficiency in factor VII (FVII) of the coagulation is a rare autosomal recessive disease, responsible for a hemorrhagic syndrome of variable intensity poorly correlated with plasma levels of FVII. This deficit is suspected in front of an isolated reduction in the rate of prothrombine and confirmed by the dosage of this factor. We report a case of congenital FVII deficiency in a patient aged 22 years, who underwent surgical treatment of nephrolithiasis. FVII deficiency was 22%, no replacement therapy was introduced to the patient, and no bleeding complications were observed in intraoperative or postoperative. In conclusion, the perioperative transfusion with fresh frozen plasma (FFP) or the contribution of FVII in a patient with a moderate deficit in FVII is not systematic, and it cannot be considered if there is a risk of bleeding or in case of deficiency of FVII.},
year = {2013}
}
TY - JOUR T1 - Congenital Deficiency in Factor VII of the Coagulation and the Anesthesia AU - Hicham Bakkali AU - Salahedine Massou AU - Fayçal Labrini AU - Khalil Mounir AU - Mustapha Bensghir AU - Hicham Azendour AU - Hicham Balkhi AU - Charqui Haimeur Y1 - 2013/11/20 PY - 2013 N1 - https://doi.org/10.11648/j.ja.20130103.12 DO - 10.11648/j.ja.20130103.12 T2 - International Journal of Anesthesia and Clinical Medicine JF - International Journal of Anesthesia and Clinical Medicine JO - International Journal of Anesthesia and Clinical Medicine SP - 24 EP - 26 PB - Science Publishing Group SN - 2997-2698 UR - https://doi.org/10.11648/j.ja.20130103.12 AB - The constitutional deficiency in factor VII (FVII) of the coagulation is a rare autosomal recessive disease, responsible for a hemorrhagic syndrome of variable intensity poorly correlated with plasma levels of FVII. This deficit is suspected in front of an isolated reduction in the rate of prothrombine and confirmed by the dosage of this factor. We report a case of congenital FVII deficiency in a patient aged 22 years, who underwent surgical treatment of nephrolithiasis. FVII deficiency was 22%, no replacement therapy was introduced to the patient, and no bleeding complications were observed in intraoperative or postoperative. In conclusion, the perioperative transfusion with fresh frozen plasma (FFP) or the contribution of FVII in a patient with a moderate deficit in FVII is not systematic, and it cannot be considered if there is a risk of bleeding or in case of deficiency of FVII. VL - 1 IS - 3 ER -
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