A Rare Case of Scalp Aplasia Cutis Congenita in a Zimbabwean Child

Brighton Valentine Nyamapfene; Tafadzwa Moreen Dube; Killion Madondoro; Aaron Musara; Kazadi Kaluile Kalangu

doi:doi:10.11648/j.ijn.20180202.14

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A Rare Case of Scalp Aplasia Cutis Congenita in a Zimbabwean Child

Brighton Valentine Nyamapfene, Tafadzwa Moreen Dube, Killion Madondoro, Aaron Musara, Kazadi Kaluile Kalangu

Published in International Journal of Neurosurgery (Volume 2, Issue 2)

Received: 23 October 2018 Accepted: 8 November 2018 Published: 4 December 2018

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Abstract

Skull and scalp defects can be a challenge in the pediatric population. They predispose to meningitis and at times catastrophic exsanguination. Aplasia Cutis Congenita is a very rare condition resulting in a variable degree of absence of epidermis and dermis. It can be associated with skull defects especially the parietal vertex. We report a case managed at our hospital of a 2 week old Zimbabwean baby with a scalp and bi-parietal bone defect present at birth. He had no other congenital anomalies. Our case was managed by rotational pedicled flap to cover the skull defect. Various methods to close the skull defects have been highlighted in literature. These may include either split skin graft or full thickness graft especially if the pericranium is viable for nutritional support. Subgaleal scoring with flap advancement can also be employed by making longitudinal incisions perpendicular to the direction of advancement. Rotational flaps are especially useful in parieto-occipital lesions like our case. Patient factors for example size of defect, location and associated skull defects determine the optimal option to be used. Aplasia Cutis Congenita is therefore a rare condition which needs a multimodal approach. Lesions above 2 cm in greatest diameter and associated skull defects should have early surgery to avoid complications like infections and hemorrhage.

Published in	International Journal of Neurosurgery (Volume 2, Issue 2)
DOI	10.11648/j.ijn.20180202.14
Page(s)	35-38
Creative Commons	This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited.
Copyright	Copyright © The Author(s), 2018. Published by Science Publishing Group

Keywords

Aplasia Cutis Congenita, Skull Defect, Scalp Reconstruction

References

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Brighton Valentine Nyamapfene, Tafadzwa Moreen Dube, Killion Madondoro, Aaron Musara, Kazadi Kaluile Kalangu. (2018). A Rare Case of Scalp Aplasia Cutis Congenita in a Zimbabwean Child. International Journal of Neurosurgery, 2(2), 35-38. https://doi.org/10.11648/j.ijn.20180202.14

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ACS Style

Brighton Valentine Nyamapfene; Tafadzwa Moreen Dube; Killion Madondoro; Aaron Musara; Kazadi Kaluile Kalangu. A Rare Case of Scalp Aplasia Cutis Congenita in a Zimbabwean Child. Int. J. Neurosurg. 2018, 2(2), 35-38. doi: 10.11648/j.ijn.20180202.14

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AMA Style

Brighton Valentine Nyamapfene, Tafadzwa Moreen Dube, Killion Madondoro, Aaron Musara, Kazadi Kaluile Kalangu. A Rare Case of Scalp Aplasia Cutis Congenita in a Zimbabwean Child. Int J Neurosurg. 2018;2(2):35-38. doi: 10.11648/j.ijn.20180202.14

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@article{10.11648/j.ijn.20180202.14,
  author = {Brighton Valentine Nyamapfene and Tafadzwa Moreen Dube and Killion Madondoro and Aaron Musara and Kazadi Kaluile Kalangu},
  title = {A Rare Case of Scalp Aplasia Cutis Congenita in a Zimbabwean Child},
  journal = {International Journal of Neurosurgery},
  volume = {2},
  number = {2},
  pages = {35-38},
  doi = {10.11648/j.ijn.20180202.14},
  url = {https://doi.org/10.11648/j.ijn.20180202.14},
  eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ijn.20180202.14},
  abstract = {Skull and scalp defects can be a challenge in the pediatric population. They predispose to meningitis and at times catastrophic exsanguination. Aplasia Cutis Congenita is a very rare condition resulting in a variable degree of absence of epidermis and dermis. It can be associated with skull defects especially the parietal vertex. We report a case managed at our hospital of a 2 week old Zimbabwean baby with a scalp and bi-parietal bone defect present at birth. He had no other congenital anomalies. Our case was managed by rotational pedicled flap to cover the skull defect. Various methods to close the skull defects have been highlighted in literature. These may include either split skin graft or full thickness graft especially if the pericranium is viable for nutritional support. Subgaleal scoring with flap advancement can also be employed by making longitudinal incisions perpendicular to the direction of advancement. Rotational flaps are especially useful in parieto-occipital lesions like our case. Patient factors for example size of defect, location and associated skull defects determine the optimal option to be used. Aplasia Cutis Congenita is therefore a rare condition which needs a multimodal approach. Lesions above 2 cm in greatest diameter and associated skull defects should have early surgery to avoid complications like infections and hemorrhage.},
 year = {2018}
}

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TY - JOUR
T1 - A Rare Case of Scalp Aplasia Cutis Congenita in a Zimbabwean Child
AU - Brighton Valentine Nyamapfene
AU - Tafadzwa Moreen Dube
AU - Killion Madondoro
AU - Aaron Musara
AU - Kazadi Kaluile Kalangu
Y1 - 2018/12/04
PY - 2018
N1 - https://doi.org/10.11648/j.ijn.20180202.14
DO - 10.11648/j.ijn.20180202.14
T2 - International Journal of Neurosurgery
JF - International Journal of Neurosurgery
JO - International Journal of Neurosurgery
SP - 35
EP - 38
PB - Science Publishing Group
SN - 2640-1959
UR - https://doi.org/10.11648/j.ijn.20180202.14
AB - Skull and scalp defects can be a challenge in the pediatric population. They predispose to meningitis and at times catastrophic exsanguination. Aplasia Cutis Congenita is a very rare condition resulting in a variable degree of absence of epidermis and dermis. It can be associated with skull defects especially the parietal vertex. We report a case managed at our hospital of a 2 week old Zimbabwean baby with a scalp and bi-parietal bone defect present at birth. He had no other congenital anomalies. Our case was managed by rotational pedicled flap to cover the skull defect. Various methods to close the skull defects have been highlighted in literature. These may include either split skin graft or full thickness graft especially if the pericranium is viable for nutritional support. Subgaleal scoring with flap advancement can also be employed by making longitudinal incisions perpendicular to the direction of advancement. Rotational flaps are especially useful in parieto-occipital lesions like our case. Patient factors for example size of defect, location and associated skull defects determine the optimal option to be used. Aplasia Cutis Congenita is therefore a rare condition which needs a multimodal approach. Lesions above 2 cm in greatest diameter and associated skull defects should have early surgery to avoid complications like infections and hemorrhage.
VL - 2
IS - 2
ER -

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Author Information

Brighton Valentine Nyamapfene

Department of Neurosurgery, University of Zimbabwe, Harare, Zimbabwe
Tafadzwa Moreen Dube

Department of Neurosurgery, University of Zimbabwe, Harare, Zimbabwe
Killion Madondoro

Department of Neurosurgery, University of Zimbabwe, Harare, Zimbabwe
Aaron Musara

Department of Neurosurgery, University of Zimbabwe, Harare, Zimbabwe
Kazadi Kaluile Kalangu

Department of Neurosurgery, University of Zimbabwe, Harare, Zimbabwe

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Plain Text BibTeX RIS

APA Style

Brighton Valentine Nyamapfene, Tafadzwa Moreen Dube, Killion Madondoro, Aaron Musara, Kazadi Kaluile Kalangu. (2018). A Rare Case of Scalp Aplasia Cutis Congenita in a Zimbabwean Child. International Journal of Neurosurgery, 2(2), 35-38. https://doi.org/10.11648/j.ijn.20180202.14

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ACS Style

Brighton Valentine Nyamapfene; Tafadzwa Moreen Dube; Killion Madondoro; Aaron Musara; Kazadi Kaluile Kalangu. A Rare Case of Scalp Aplasia Cutis Congenita in a Zimbabwean Child. Int. J. Neurosurg. 2018, 2(2), 35-38. doi: 10.11648/j.ijn.20180202.14

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AMA Style

Brighton Valentine Nyamapfene, Tafadzwa Moreen Dube, Killion Madondoro, Aaron Musara, Kazadi Kaluile Kalangu. A Rare Case of Scalp Aplasia Cutis Congenita in a Zimbabwean Child. Int J Neurosurg. 2018;2(2):35-38. doi: 10.11648/j.ijn.20180202.14

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@article{10.11648/j.ijn.20180202.14,
  author = {Brighton Valentine Nyamapfene and Tafadzwa Moreen Dube and Killion Madondoro and Aaron Musara and Kazadi Kaluile Kalangu},
  title = {A Rare Case of Scalp Aplasia Cutis Congenita in a Zimbabwean Child},
  journal = {International Journal of Neurosurgery},
  volume = {2},
  number = {2},
  pages = {35-38},
  doi = {10.11648/j.ijn.20180202.14},
  url = {https://doi.org/10.11648/j.ijn.20180202.14},
  eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ijn.20180202.14},
  abstract = {Skull and scalp defects can be a challenge in the pediatric population. They predispose to meningitis and at times catastrophic exsanguination. Aplasia Cutis Congenita is a very rare condition resulting in a variable degree of absence of epidermis and dermis. It can be associated with skull defects especially the parietal vertex. We report a case managed at our hospital of a 2 week old Zimbabwean baby with a scalp and bi-parietal bone defect present at birth. He had no other congenital anomalies. Our case was managed by rotational pedicled flap to cover the skull defect. Various methods to close the skull defects have been highlighted in literature. These may include either split skin graft or full thickness graft especially if the pericranium is viable for nutritional support. Subgaleal scoring with flap advancement can also be employed by making longitudinal incisions perpendicular to the direction of advancement. Rotational flaps are especially useful in parieto-occipital lesions like our case. Patient factors for example size of defect, location and associated skull defects determine the optimal option to be used. Aplasia Cutis Congenita is therefore a rare condition which needs a multimodal approach. Lesions above 2 cm in greatest diameter and associated skull defects should have early surgery to avoid complications like infections and hemorrhage.},
 year = {2018}
}

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