Total anomalus pulmonary venous drainage refers to the absence of connection of the four pulmonary veins to the left atrium. This anomaly is often associated with atrial septal defect This is a rare malformation, with total forms accounting for 0.4% of all congenital heart defects, while partial forms account for between 0.6 and 0.7%. Diagnosis is a delicate matter, made by cardiac ultrasound performed by an experienced operator. The aim of this work was to establish the characteristics of this pathology, to determine the operative indications, and to evaluate the operative results. We report the case of the first complete cure of total anomalous pulmonary venous return at the Festoc center in Bamako. The patient was 08 years old and was initially referred to us for management of a sinus venosus atrial septal defect with symptoms of precordialgia and stage 2 to 3 dyspnoea. Examination revealed a mesocardial systolic murmur. Cardiac ultrasound revealed a 38 mm wide atrial septal defect sinus veinosus with no superior vena cava. Surgical exploration revealed a single atrium with total abnormal pulmonary venous return. Given the local team's lack of experience with this complex congenital anomaly, a collegial decision was taken to enlarge the ASV. Three weeks later, the patient underwent a repeat operation under extracorporeal circulation after an angioscan scan had revealed the collector. Surgical exploration revealed a single atrium with a small left atrium. The collector ended at the TVI. We re-implanted the collector in the left atrium and ligated the TVI. Pulmonary venous return anomalies are rare conditions and represent a heterogeneous group of cardiovascular malformations. Their incidence is estimated at 0.4-0.7% of all congenital heart defects. Their management requires a certain level of logistical organization and technical expertise, which can be envisaged in developing countries. North-South cooperation is also a very important aspect in the ongoing training of medical staff and the management of certain complex cardiopathies.
Published in | International Journal of Cardiovascular and Thoracic Surgery (Volume 9, Issue 3) |
DOI | 10.11648/j.ijcts.20230903.14 |
Page(s) | 36-39 |
Creative Commons |
This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited. |
Copyright |
Copyright © The Author(s), 2023. Published by Science Publishing Group |
Anomalous, Pulmonary Venous, Repair, Bamako
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APA Style
Baba Ibrahima Diarra, Modibo Doumbia, Mamadou Touré, Sanoussy Daffe, Bakary Coulibaly, et al. (2023). Total Anomalus Pulmonary Venous Connection: About a Case Operated on at the Andre Festoc Center of Bamako. International Journal of Cardiovascular and Thoracic Surgery, 9(3), 36-39. https://doi.org/10.11648/j.ijcts.20230903.14
ACS Style
Baba Ibrahima Diarra; Modibo Doumbia; Mamadou Touré; Sanoussy Daffe; Bakary Coulibaly, et al. Total Anomalus Pulmonary Venous Connection: About a Case Operated on at the Andre Festoc Center of Bamako. Int. J. Cardiovasc. Thorac. Surg. 2023, 9(3), 36-39. doi: 10.11648/j.ijcts.20230903.14
AMA Style
Baba Ibrahima Diarra, Modibo Doumbia, Mamadou Touré, Sanoussy Daffe, Bakary Coulibaly, et al. Total Anomalus Pulmonary Venous Connection: About a Case Operated on at the Andre Festoc Center of Bamako. Int J Cardiovasc Thorac Surg. 2023;9(3):36-39. doi: 10.11648/j.ijcts.20230903.14
@article{10.11648/j.ijcts.20230903.14, author = {Baba Ibrahima Diarra and Modibo Doumbia and Mamadou Touré and Sanoussy Daffe and Bakary Coulibaly and Oumar Doucouré and Siriman Koita and Diallo Binta and Salia Traoré and Mahamadoune Coulibaly and Mamadou Bocary Diarra and Birama Togola and Seydou Togo and Moussa Abdoulaye Ouattara and Sadio Yena and Paul Neuville and Guy Fernandez and Bina Nadjeeboulah and Erwan Flecher and Thiery Langanay and Alain Deloche}, title = {Total Anomalus Pulmonary Venous Connection: About a Case Operated on at the Andre Festoc Center of Bamako}, journal = {International Journal of Cardiovascular and Thoracic Surgery}, volume = {9}, number = {3}, pages = {36-39}, doi = {10.11648/j.ijcts.20230903.14}, url = {https://doi.org/10.11648/j.ijcts.20230903.14}, eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ijcts.20230903.14}, abstract = {Total anomalus pulmonary venous drainage refers to the absence of connection of the four pulmonary veins to the left atrium. This anomaly is often associated with atrial septal defect This is a rare malformation, with total forms accounting for 0.4% of all congenital heart defects, while partial forms account for between 0.6 and 0.7%. Diagnosis is a delicate matter, made by cardiac ultrasound performed by an experienced operator. The aim of this work was to establish the characteristics of this pathology, to determine the operative indications, and to evaluate the operative results. We report the case of the first complete cure of total anomalous pulmonary venous return at the Festoc center in Bamako. The patient was 08 years old and was initially referred to us for management of a sinus venosus atrial septal defect with symptoms of precordialgia and stage 2 to 3 dyspnoea. Examination revealed a mesocardial systolic murmur. Cardiac ultrasound revealed a 38 mm wide atrial septal defect sinus veinosus with no superior vena cava. Surgical exploration revealed a single atrium with total abnormal pulmonary venous return. Given the local team's lack of experience with this complex congenital anomaly, a collegial decision was taken to enlarge the ASV. Three weeks later, the patient underwent a repeat operation under extracorporeal circulation after an angioscan scan had revealed the collector. Surgical exploration revealed a single atrium with a small left atrium. The collector ended at the TVI. We re-implanted the collector in the left atrium and ligated the TVI. Pulmonary venous return anomalies are rare conditions and represent a heterogeneous group of cardiovascular malformations. Their incidence is estimated at 0.4-0.7% of all congenital heart defects. Their management requires a certain level of logistical organization and technical expertise, which can be envisaged in developing countries. North-South cooperation is also a very important aspect in the ongoing training of medical staff and the management of certain complex cardiopathies.}, year = {2023} }
TY - JOUR T1 - Total Anomalus Pulmonary Venous Connection: About a Case Operated on at the Andre Festoc Center of Bamako AU - Baba Ibrahima Diarra AU - Modibo Doumbia AU - Mamadou Touré AU - Sanoussy Daffe AU - Bakary Coulibaly AU - Oumar Doucouré AU - Siriman Koita AU - Diallo Binta AU - Salia Traoré AU - Mahamadoune Coulibaly AU - Mamadou Bocary Diarra AU - Birama Togola AU - Seydou Togo AU - Moussa Abdoulaye Ouattara AU - Sadio Yena AU - Paul Neuville AU - Guy Fernandez AU - Bina Nadjeeboulah AU - Erwan Flecher AU - Thiery Langanay AU - Alain Deloche Y1 - 2023/06/29 PY - 2023 N1 - https://doi.org/10.11648/j.ijcts.20230903.14 DO - 10.11648/j.ijcts.20230903.14 T2 - International Journal of Cardiovascular and Thoracic Surgery JF - International Journal of Cardiovascular and Thoracic Surgery JO - International Journal of Cardiovascular and Thoracic Surgery SP - 36 EP - 39 PB - Science Publishing Group SN - 2575-4882 UR - https://doi.org/10.11648/j.ijcts.20230903.14 AB - Total anomalus pulmonary venous drainage refers to the absence of connection of the four pulmonary veins to the left atrium. This anomaly is often associated with atrial septal defect This is a rare malformation, with total forms accounting for 0.4% of all congenital heart defects, while partial forms account for between 0.6 and 0.7%. Diagnosis is a delicate matter, made by cardiac ultrasound performed by an experienced operator. The aim of this work was to establish the characteristics of this pathology, to determine the operative indications, and to evaluate the operative results. We report the case of the first complete cure of total anomalous pulmonary venous return at the Festoc center in Bamako. The patient was 08 years old and was initially referred to us for management of a sinus venosus atrial septal defect with symptoms of precordialgia and stage 2 to 3 dyspnoea. Examination revealed a mesocardial systolic murmur. Cardiac ultrasound revealed a 38 mm wide atrial septal defect sinus veinosus with no superior vena cava. Surgical exploration revealed a single atrium with total abnormal pulmonary venous return. Given the local team's lack of experience with this complex congenital anomaly, a collegial decision was taken to enlarge the ASV. Three weeks later, the patient underwent a repeat operation under extracorporeal circulation after an angioscan scan had revealed the collector. Surgical exploration revealed a single atrium with a small left atrium. The collector ended at the TVI. We re-implanted the collector in the left atrium and ligated the TVI. Pulmonary venous return anomalies are rare conditions and represent a heterogeneous group of cardiovascular malformations. Their incidence is estimated at 0.4-0.7% of all congenital heart defects. Their management requires a certain level of logistical organization and technical expertise, which can be envisaged in developing countries. North-South cooperation is also a very important aspect in the ongoing training of medical staff and the management of certain complex cardiopathies. VL - 9 IS - 3 ER -