Interrupted Aortic Arch is a rare congenital anomaly with an incidence of 2 per 100,000 live births. It is almost always (95-97%) associated with structural abnormality like VSD. Interrupted Aortic Arch is usually diagnosed soon after birth, and when left untreated results in 90% mortality at a median age of 4 days. Isolated IAA is a very rare entity. Substantial collateral circulation must be present to maintain flow and enable survival. Conventional surgical repair is a challenge due to extensive collateral circulation in patients who have survived to adulthood. Here, we report a patient with an isolated IAA without any associated defect who survived into third decade. The patient presented with complaints of palpitations, uncontrolled hypertension, and weakness in lower limbs and on evaluation, he had isolated Interrupted Aortic Arch. We managed to do an Extra anatomical Bypass graft from ascending aorta to descending aorta on a beating heart with minimal risk. The procedure was done through median sternotomy to avoid the damage to collaterals when approached through thoracotomy.
| Published in | International Journal of Cardiovascular and Thoracic Surgery (Volume 5, Issue 5) |
| DOI | 10.11648/j.ijcts.20190505.11 |
| Page(s) | 72-75 |
| Creative Commons |
This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited. |
| Copyright |
Copyright © The Author(s), 2019. Published by Science Publishing Group |
Interrupted Aortic Arch, Extra Anatomical Bypass, Sternotomy, Collaterals, IAA
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APA Style
Anirudh Kumar Paidi, Palli Venkata Naresh Kumar, Madhava Rao Midhe, Ravi Kiran Mamidala, Venkat Reddy Navuluri. (2019). Extra Anatomic Repair of Interrupted Aortic Arch. International Journal of Cardiovascular and Thoracic Surgery, 5(5), 72-75. https://doi.org/10.11648/j.ijcts.20190505.11
ACS Style
Anirudh Kumar Paidi; Palli Venkata Naresh Kumar; Madhava Rao Midhe; Ravi Kiran Mamidala; Venkat Reddy Navuluri. Extra Anatomic Repair of Interrupted Aortic Arch. Int. J. Cardiovasc. Thorac. Surg. 2019, 5(5), 72-75. doi: 10.11648/j.ijcts.20190505.11
AMA Style
Anirudh Kumar Paidi, Palli Venkata Naresh Kumar, Madhava Rao Midhe, Ravi Kiran Mamidala, Venkat Reddy Navuluri. Extra Anatomic Repair of Interrupted Aortic Arch. Int J Cardiovasc Thorac Surg. 2019;5(5):72-75. doi: 10.11648/j.ijcts.20190505.11
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Download@article{10.11648/j.ijcts.20190505.11,
author = {Anirudh Kumar Paidi and Palli Venkata Naresh Kumar and Madhava Rao Midhe and Ravi Kiran Mamidala and Venkat Reddy Navuluri},
title = {Extra Anatomic Repair of Interrupted Aortic Arch},
journal = {International Journal of Cardiovascular and Thoracic Surgery},
volume = {5},
number = {5},
pages = {72-75},
doi = {10.11648/j.ijcts.20190505.11},
url = {https://doi.org/10.11648/j.ijcts.20190505.11},
eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ijcts.20190505.11},
abstract = {Interrupted Aortic Arch is a rare congenital anomaly with an incidence of 2 per 100,000 live births. It is almost always (95-97%) associated with structural abnormality like VSD. Interrupted Aortic Arch is usually diagnosed soon after birth, and when left untreated results in 90% mortality at a median age of 4 days. Isolated IAA is a very rare entity. Substantial collateral circulation must be present to maintain flow and enable survival. Conventional surgical repair is a challenge due to extensive collateral circulation in patients who have survived to adulthood. Here, we report a patient with an isolated IAA without any associated defect who survived into third decade. The patient presented with complaints of palpitations, uncontrolled hypertension, and weakness in lower limbs and on evaluation, he had isolated Interrupted Aortic Arch. We managed to do an Extra anatomical Bypass graft from ascending aorta to descending aorta on a beating heart with minimal risk. The procedure was done through median sternotomy to avoid the damage to collaterals when approached through thoracotomy.},
year = {2019}
}
TY - JOUR T1 - Extra Anatomic Repair of Interrupted Aortic Arch AU - Anirudh Kumar Paidi AU - Palli Venkata Naresh Kumar AU - Madhava Rao Midhe AU - Ravi Kiran Mamidala AU - Venkat Reddy Navuluri Y1 - 2019/11/04 PY - 2019 N1 - https://doi.org/10.11648/j.ijcts.20190505.11 DO - 10.11648/j.ijcts.20190505.11 T2 - International Journal of Cardiovascular and Thoracic Surgery JF - International Journal of Cardiovascular and Thoracic Surgery JO - International Journal of Cardiovascular and Thoracic Surgery SP - 72 EP - 75 PB - Science Publishing Group SN - 2575-4882 UR - https://doi.org/10.11648/j.ijcts.20190505.11 AB - Interrupted Aortic Arch is a rare congenital anomaly with an incidence of 2 per 100,000 live births. It is almost always (95-97%) associated with structural abnormality like VSD. Interrupted Aortic Arch is usually diagnosed soon after birth, and when left untreated results in 90% mortality at a median age of 4 days. Isolated IAA is a very rare entity. Substantial collateral circulation must be present to maintain flow and enable survival. Conventional surgical repair is a challenge due to extensive collateral circulation in patients who have survived to adulthood. Here, we report a patient with an isolated IAA without any associated defect who survived into third decade. The patient presented with complaints of palpitations, uncontrolled hypertension, and weakness in lower limbs and on evaluation, he had isolated Interrupted Aortic Arch. We managed to do an Extra anatomical Bypass graft from ascending aorta to descending aorta on a beating heart with minimal risk. The procedure was done through median sternotomy to avoid the damage to collaterals when approached through thoracotomy. VL - 5 IS - 5 ER -
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