Background Pulmonary arterial hypertension (PAH) is a serious complication of unrepaired congenital heart disease (CHD). The aim of this retrospective study was to evaluate the management of PAH associated with CHD (APAH-CHD) in the Iraqi Center for Heart Disease, Baghdad. Methodology Twenty children with APAH-CHD were surgically treated over 2 years (1st June 2013 to 1st June 2015).Clinical evaluation was followed by chest radiography and transthoracic echocardiography (TTE). Suspected inoperable patients were subjected to cardiac catheterization and Oxygen test. Total surgical correction was elected in children with mild to moderate PAH while young children with low body weight and severe PAH were offered pulmonary artery banding (PAB) reducing PA pressure to 50% of the systemic pressure. All patients were looked after carefully in the ICU. TTE was used in the follow up. Results There were 12 females (F: M=1.5:1) The ages ranged between 4 and 84 months with a mean of 16.4 ± 20.1 months. Seventy % were infants. Five patients (25%) underwent cardiac catheterization. Ventricular septal defect was the commonest underlying anomaly (90%). Twelve patients had full correction and they were significantly older than those treated by PAB. Three totally corrected kids died (25% death) whereas no child died after PAB. Pulmonary hypertensive crisis was accused once. The remaining 17 patients were followed up for 6-18 months; 14 were alive when this paper was written. Conclusion PAB may be a good option for the very young and sick children who might not tolerate a lengthy total correction.
| Published in | International Journal of Cardiovascular and Thoracic Surgery (Volume 2, Issue 4) |
| DOI | 10.11648/j.ijcts.20160204.11 |
| Page(s) | 15-21 |
| Creative Commons |
This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited. |
| Copyright |
Copyright © The Author(s), 2016. Published by Science Publishing Group |
Pulmonary Arterial Hypertension, Associated, Congenital Heart Disease, Children, Eisenmenger’s Syndrome, Pulmonary Artery Banding, Total Correction
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APA Style
Abdulsalam Y. Taha, Ahmed M. Ibraheem. (2016). Management of Pulmonary Arterial Hypertension Associated with Congenital Heart Disease in Children. International Journal of Cardiovascular and Thoracic Surgery, 2(4), 15-21. https://doi.org/10.11648/j.ijcts.20160204.11
ACS Style
Abdulsalam Y. Taha; Ahmed M. Ibraheem. Management of Pulmonary Arterial Hypertension Associated with Congenital Heart Disease in Children. Int. J. Cardiovasc. Thorac. Surg. 2016, 2(4), 15-21. doi: 10.11648/j.ijcts.20160204.11
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Download@article{10.11648/j.ijcts.20160204.11,
author = {Abdulsalam Y. Taha and Ahmed M. Ibraheem},
title = {Management of Pulmonary Arterial Hypertension Associated with Congenital Heart Disease in Children},
journal = {International Journal of Cardiovascular and Thoracic Surgery},
volume = {2},
number = {4},
pages = {15-21},
doi = {10.11648/j.ijcts.20160204.11},
url = {https://doi.org/10.11648/j.ijcts.20160204.11},
eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ijcts.20160204.11},
abstract = {Background Pulmonary arterial hypertension (PAH) is a serious complication of unrepaired congenital heart disease (CHD). The aim of this retrospective study was to evaluate the management of PAH associated with CHD (APAH-CHD) in the Iraqi Center for Heart Disease, Baghdad. Methodology Twenty children with APAH-CHD were surgically treated over 2 years (1st June 2013 to 1st June 2015).Clinical evaluation was followed by chest radiography and transthoracic echocardiography (TTE). Suspected inoperable patients were subjected to cardiac catheterization and Oxygen test. Total surgical correction was elected in children with mild to moderate PAH while young children with low body weight and severe PAH were offered pulmonary artery banding (PAB) reducing PA pressure to 50% of the systemic pressure. All patients were looked after carefully in the ICU. TTE was used in the follow up. Results There were 12 females (F: M=1.5:1) The ages ranged between 4 and 84 months with a mean of 16.4 ± 20.1 months. Seventy % were infants. Five patients (25%) underwent cardiac catheterization. Ventricular septal defect was the commonest underlying anomaly (90%). Twelve patients had full correction and they were significantly older than those treated by PAB. Three totally corrected kids died (25% death) whereas no child died after PAB. Pulmonary hypertensive crisis was accused once. The remaining 17 patients were followed up for 6-18 months; 14 were alive when this paper was written. Conclusion PAB may be a good option for the very young and sick children who might not tolerate a lengthy total correction.},
year = {2016}
}
TY - JOUR T1 - Management of Pulmonary Arterial Hypertension Associated with Congenital Heart Disease in Children AU - Abdulsalam Y. Taha AU - Ahmed M. Ibraheem Y1 - 2016/10/11 PY - 2016 N1 - https://doi.org/10.11648/j.ijcts.20160204.11 DO - 10.11648/j.ijcts.20160204.11 T2 - International Journal of Cardiovascular and Thoracic Surgery JF - International Journal of Cardiovascular and Thoracic Surgery JO - International Journal of Cardiovascular and Thoracic Surgery SP - 15 EP - 21 PB - Science Publishing Group SN - 2575-4882 UR - https://doi.org/10.11648/j.ijcts.20160204.11 AB - Background Pulmonary arterial hypertension (PAH) is a serious complication of unrepaired congenital heart disease (CHD). The aim of this retrospective study was to evaluate the management of PAH associated with CHD (APAH-CHD) in the Iraqi Center for Heart Disease, Baghdad. Methodology Twenty children with APAH-CHD were surgically treated over 2 years (1st June 2013 to 1st June 2015).Clinical evaluation was followed by chest radiography and transthoracic echocardiography (TTE). Suspected inoperable patients were subjected to cardiac catheterization and Oxygen test. Total surgical correction was elected in children with mild to moderate PAH while young children with low body weight and severe PAH were offered pulmonary artery banding (PAB) reducing PA pressure to 50% of the systemic pressure. All patients were looked after carefully in the ICU. TTE was used in the follow up. Results There were 12 females (F: M=1.5:1) The ages ranged between 4 and 84 months with a mean of 16.4 ± 20.1 months. Seventy % were infants. Five patients (25%) underwent cardiac catheterization. Ventricular septal defect was the commonest underlying anomaly (90%). Twelve patients had full correction and they were significantly older than those treated by PAB. Three totally corrected kids died (25% death) whereas no child died after PAB. Pulmonary hypertensive crisis was accused once. The remaining 17 patients were followed up for 6-18 months; 14 were alive when this paper was written. Conclusion PAB may be a good option for the very young and sick children who might not tolerate a lengthy total correction. VL - 2 IS - 4 ER -
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