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Joint Hypermobility Syndrome: A Narrative Review

Received: 1 May 2023     Accepted: 15 May 2023     Published: 25 May 2023
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Abstract

Joint hypermobility syndrome (JHS) is a complex connective tissue disorder characterized by excessive joint mobility and chronic musculoskeletal pain. The condition extends beyond the joints and can affect various systems such as the skin, gastrointestinal tract, neurological system, and cardiovascular system, necessitating a multidisciplinary approach to optimize care. Notably, the prevalence of JHS is higher in young individuals, females, and those of Asian descent. Despite being a common condition, JHS is frequently underdiagnosed, resulting in persistent pain and disability. In order to diagnose JHS, it is necessary to rule out the presence of any consistent feature that indicates the existence of other connective tissue disorders that partially overlap with it, including Marfan and Ehlers-Danlos syndromes. A thorough clinical assessment, coupled with the application of the Brighton Criteria, can aid in making an accurate diagnosis. Management of JHS poses significant challenges and typically involves symptomatic treatment, including physiotherapy, rehabilitation, and pharmacological therapy. Additionally, a multidisciplinary approach, including collaboration with different specialists, is vital. Further research is needed to improve our understanding of JHS and develop interventions based on solid evidence. However, with comprehensive management strategies, individuals with JHS can achieve better pain control and improved function, enabling them to lead more fulfilling lives.

Published in American Journal of Internal Medicine (Volume 11, Issue 3)
DOI 10.11648/j.ajim.20231103.12
Page(s) 35-40
Creative Commons

This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited.

Copyright

Copyright © The Author(s), 2023. Published by Science Publishing Group

Keywords

Hypermobility Syndrome, Ehlers-Danlos Syndrome, Joint Pain, Chronic Pain

References
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Cite This Article
  • APA Style

    Jobson Lopes de Oliveira, Igor Albuquerque Nogueira, Camila Távora Nogueira, Saulo Venicius Parente Lopes, Gabriela Silva Teles, et al. (2023). Joint Hypermobility Syndrome: A Narrative Review. American Journal of Internal Medicine, 11(3), 35-40. https://doi.org/10.11648/j.ajim.20231103.12

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    ACS Style

    Jobson Lopes de Oliveira; Igor Albuquerque Nogueira; Camila Távora Nogueira; Saulo Venicius Parente Lopes; Gabriela Silva Teles, et al. Joint Hypermobility Syndrome: A Narrative Review. Am. J. Intern. Med. 2023, 11(3), 35-40. doi: 10.11648/j.ajim.20231103.12

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    AMA Style

    Jobson Lopes de Oliveira, Igor Albuquerque Nogueira, Camila Távora Nogueira, Saulo Venicius Parente Lopes, Gabriela Silva Teles, et al. Joint Hypermobility Syndrome: A Narrative Review. Am J Intern Med. 2023;11(3):35-40. doi: 10.11648/j.ajim.20231103.12

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  • @article{10.11648/j.ajim.20231103.12,
      author = {Jobson Lopes de Oliveira and Igor Albuquerque Nogueira and Camila Távora Nogueira and Saulo Venicius Parente Lopes and Gabriela Silva Teles and Raul Sancho de Carvalho Rocha and Pedro Iughetti Morais and Ana Beatriz Cordeiro Carvalho and Pedro Henrique de Santana Pereira and David Johnson Pinheiro Alencar},
      title = {Joint Hypermobility Syndrome: A Narrative Review},
      journal = {American Journal of Internal Medicine},
      volume = {11},
      number = {3},
      pages = {35-40},
      doi = {10.11648/j.ajim.20231103.12},
      url = {https://doi.org/10.11648/j.ajim.20231103.12},
      eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ajim.20231103.12},
      abstract = {Joint hypermobility syndrome (JHS) is a complex connective tissue disorder characterized by excessive joint mobility and chronic musculoskeletal pain. The condition extends beyond the joints and can affect various systems such as the skin, gastrointestinal tract, neurological system, and cardiovascular system, necessitating a multidisciplinary approach to optimize care. Notably, the prevalence of JHS is higher in young individuals, females, and those of Asian descent. Despite being a common condition, JHS is frequently underdiagnosed, resulting in persistent pain and disability. In order to diagnose JHS, it is necessary to rule out the presence of any consistent feature that indicates the existence of other connective tissue disorders that partially overlap with it, including Marfan and Ehlers-Danlos syndromes. A thorough clinical assessment, coupled with the application of the Brighton Criteria, can aid in making an accurate diagnosis. Management of JHS poses significant challenges and typically involves symptomatic treatment, including physiotherapy, rehabilitation, and pharmacological therapy. Additionally, a multidisciplinary approach, including collaboration with different specialists, is vital. Further research is needed to improve our understanding of JHS and develop interventions based on solid evidence. However, with comprehensive management strategies, individuals with JHS can achieve better pain control and improved function, enabling them to lead more fulfilling lives.},
     year = {2023}
    }
    

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    T1  - Joint Hypermobility Syndrome: A Narrative Review
    AU  - Jobson Lopes de Oliveira
    AU  - Igor Albuquerque Nogueira
    AU  - Camila Távora Nogueira
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    AU  - Raul Sancho de Carvalho Rocha
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    AB  - Joint hypermobility syndrome (JHS) is a complex connective tissue disorder characterized by excessive joint mobility and chronic musculoskeletal pain. The condition extends beyond the joints and can affect various systems such as the skin, gastrointestinal tract, neurological system, and cardiovascular system, necessitating a multidisciplinary approach to optimize care. Notably, the prevalence of JHS is higher in young individuals, females, and those of Asian descent. Despite being a common condition, JHS is frequently underdiagnosed, resulting in persistent pain and disability. In order to diagnose JHS, it is necessary to rule out the presence of any consistent feature that indicates the existence of other connective tissue disorders that partially overlap with it, including Marfan and Ehlers-Danlos syndromes. A thorough clinical assessment, coupled with the application of the Brighton Criteria, can aid in making an accurate diagnosis. Management of JHS poses significant challenges and typically involves symptomatic treatment, including physiotherapy, rehabilitation, and pharmacological therapy. Additionally, a multidisciplinary approach, including collaboration with different specialists, is vital. Further research is needed to improve our understanding of JHS and develop interventions based on solid evidence. However, with comprehensive management strategies, individuals with JHS can achieve better pain control and improved function, enabling them to lead more fulfilling lives.
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Author Information
  • Departament of Internal Medicine, Faculty of Medicine, Federal University of Ceará, Fortaleza, Brazil

  • Departament of Internal Medicine, Faculty of Medicine, Federal University of Ceará, Fortaleza, Brazil

  • Departament of Internal Medicine, Faculty of Medicine, Christus University Center (Unichristus), Fortaleza, Brazil

  • Departament of Internal Medicine, Faculty of Medicine, University of Fortaleza (Unifor), Fortaleza, Brazil

  • Albert Sabin Children's Hospital, Fortaleza, Brazil

  • Departament of Internal Medicine, Faculty of Medicine, Christus University Center (Unichristus), Fortaleza, Brazil

  • Departament of Internal Medicine, Faculty of Medicine, Christus University Center (Unichristus), Fortaleza, Brazil

  • Departament of Internal Medicine, Faculty of Medicine, Christus University Center (Unichristus), Fortaleza, Brazil

  • Departament of Internal Medicine, Faculty of Medicine, Christus University Center (Unichristus), Fortaleza, Brazil

  • Departament of Internal Medicine, Faculty of Medicine, Christus University Center (Unichristus), Fortaleza, Brazil

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